Osteopoikilosis - associated with dwarfism and presenting as painful joint effusion

Benjamin Alex; Sanal Kumar; Rajeev K.; Suvin R.; Dhanesh S.

doi:10.18203/issn.2455-4510.IntJResOrthop20231405

Authors

Benjamin Alex Department of Orthopaedics, ESIC Government Hospital, Ezhukone, Kollam District, Kerala, India
Sanal Kumar Department of Orthopaedics, ESIC Government Hospital, Ezhukone, Kollam District, Kerala, India
Rajeev K. Department of Orthopaedics, ESIC Government Hospital, Ezhukone, Kollam District, Kerala, India
Suvin R. Department of Orthopaedics, ESIC Government Hospital, Ezhukone, Kollam District, Kerala, India
Dhanesh S. Department of Orthopaedics, ESIC Government Hospital, Ezhukone, Kollam District, Kerala, India

DOI:

https://doi.org/10.18203/issn.2455-4510.IntJResOrthop20231405

Keywords:

Osteopoikilosis, Spotted bone disease, Sclerotic bone dysplasia

Abstract

Osteopoikilosis is usually asymptomatic with only 15-20% patient having pain or joint effusion. Sclerotic dysplasia has multiple differential diagnosis including benign and malignant etiology. Characteristic features of symmetric, round to oval sclerotic lesions in multiple joints with axial skeleton sparing, no cortical erosion, normal clinical and blood investigations help differentiate osteopikilosis from critical malignant sclerotic pathology.

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